Congenital Vascular Anomalies: A Case Report

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Submit Manuscript | http://medcraveonline.com sometimes it may occur as an autosomal dominant trait [1,2]. Klippel-Trenaunay-Weber Syndrome is a cutaneous vascular malformation affecting the development of blood vessels, soft tissues and bones [3]. This is a non-heritable disorder which is present at birth and usually involves lower limb but may involve more than one limb and a portion of the trunk and face [4]. Most people with Klippel-Trenaunay syndrome are born with a port wine stain [5]. The port-wine stain usually covers part of one limb [6]. The affected area may become lighter or darker with age. Klippel-Trenaunay syndrome is also associated with overgrowth of bones and soft tissue beginning in infancy [5]. Klippel-Trenaunay syndrome is estimated to affect at least 1 in 100,000 people worldwide [7]. It affects male and female equally, and not limited to any racial group [8]. Klippel-TrenaunayWeber syndrome is a rare congenital defect; that is why we are reporting this case. Recently International Society for the Study of Vascular Anomalies classified Vascular Anomalies and labelled Klippel-Trenaunay-Weber Syndrome as CM + VM +/LM + limb overgrowth.

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تاریخ انتشار 2015